Special Issue

Topic: Advances in the Management of Cardiac Amyloidosis
Guest Editors
Prof. Livi Ugolino
Department of Cardiothoracic Surgery, Azienda Sanitaria Universitaria Integrata, Udine, Italy; Department of Medical Area, University of Udine, Udine, Italy.
Special Issue Introduction
Systemic amyloidosis is a rare haematologic disorder where fibrils of misfolded proteins acquire a b-pleated sheet conformation, form amyloid fibril proteins, and begin to infiltrate tissues leading to organ failure. At least 30 different proteins have been reported to produce amyloid fibrils, but two types are more capable of affecting the heart, such as light-chain (AL) amyloidosis and transthyretin-related (TTR) amyloidosis, as hereditary or acquired form. The heart involvement due to the extracellular protein fibril deposition in the myocardium could appear with several manifestations, ranging from conduction-system disease to atrial fibrillation, sudden cardiac death or restrictive cardiomyopathy and heart failure, thus conditioning the stage and prognosis of the entire disease. Recently, significant progress has been made in the treatment of amyloid cardiomyopathy, and these promising results have already opened new chances for these patients. This Special Issue has two main objectives: (1) to provide the readers, through thoughtful review articles, a comprehensive state-of-art of the current knowledge about cardiac amyloidosis; (2) to stimulate researchers to share their experience in this field, since the overall contributions could open new borders in such rare diseases, as cardiac amyloidosis.
Keywords
Cardiac amyloidosis, light chain cardiac amyloidosis, transthyretin amyloid cardiomyopathy, wild type TTR amyloidosis, hereditary TTR amyloidosis, heart failure, heart transplantation
Submission Deadline
29 Apr 2021
Submission Information
For Author Instructions, please refer to https://www.oaepublish.com/vp/author_instructions
For Online Submission, please login at https://www.oaecenter.com/login?JournalId=vp&IssueId=vp210430546
Submission Deadline: 30 Apr 2021
Contacts: Grace Zheng, Assistant Editor, [email protected]
Published Articles
Cardiac amyloidosis: the pathologist’s point of view
Open Access Review 16 Oct 2022
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Clinical translation of genetic testing in TTR Amyloidosis: genotype-phenotype correlations, management of asymptomatic carriers and familial screening
Open Access Review 29 Sep 2022
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Heart transplantation in cardiac amyloidosis
Open Access Review 31 Jul 2022
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The changing perspective on cardiac amyloidosis in the modern era
Open Access Editorial 31 Jul 2022
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Grey zones in the supportive treatments of cardiac amyloidosis
Open Access Review 31 May 2022
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Cardiac amyloidosis: a changing epidemiology with open challenges
Open Access Review 12 May 2022
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Clinical application of cardiac scintigraphy with bone tracers: controversies and pitfalls in cardiac amyloidosis
Open Access Review 4 Mar 2022
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Mid-basal left ventricular longitudinal dysfunction as a prognostic marker in mutated transthyretin-related cardiac amyloidosis
Open Access Original Article 16 Feb 2022
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Disclosing the cardiomyopathic substrate within the heart muscles in amyloidosis by cardiac magnetic resonance: diagnostic and prognostic implications
Open Access Review 16 Feb 2022
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Recent advances in the pharmacotherapy of TTR amyloidosis of the heart
Open Access Review 24 Oct 2021
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Interpreting signals from the peripheral nerve in amyloidosis: a call for action
Open Access Review 20 Jul 2021
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Nuclear medicine techniques for the diagnosis of cardiac amyloidosis: the state of the art
Open Access Review 4 Jul 2021
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