fig1
Figure 1. CL levels are reduced and trioleoyl-MLCL and citrate synthase activity elevated in BTHS lymphoblasts. Quantification of the major CL. (A) and Major MLCL (B) Fatty acyl molecular species in age-matched control and BTHS lymphoblasts as described in Materials and Methods. (C) Mitochondrial fractions were prepared from age-matched control and BTHS lymphoblasts and citrate synthase activity determined as described in Materials and Methods. Data represent the mean + SD, n = 4. #P < 0.001; **P < 0.01;
