REFERENCES
2. Syamasundar Rao P. Fontan operation: a comprehensive review. In: S. Firstenberg M, Khan I, editors. Advances in complex valvular disease. IntechOpen; 2021.
3. Cordina RL, O'Meagher S, Karmali A, et al. Resistance training improves cardiac output, exercise capacity and tolerance to positive airway pressure in Fontan physiology. Int J Cardiol 2013;168:780-8.
4. McCrindle BW, Williams RV, Mital S, et al. Physical activity levels in children and adolescents are reduced after the Fontan procedure, independent of exercise capacity, and are associated with lower perceived general health. Arch Dis Child 2007;92:509-14.
5. Ong L, Nolan RP, Irvine J, Kovacs AH. Parental overprotection and heart-focused anxiety in adults with congenital heart disease. Int J Behav Med 2011;18:260-7.
6. Argiento P, Chesler N, Mulè M, et al. Exercise stress echocardiography for the study of the pulmonary circulation. Eur Respir J 2010;35:1273-8.
7. Stickland MK, Welsh RC, Petersen SR, et al. Does fitness level modulate the cardiovascular hemodynamic response to exercise? J Appl Physiol (1985) 2006;100:1895-901.
8. Hsia TY, Khambadkone S, Redington AN, Migliavacca F, Deanfield JE, de Leval MR. Effects of respiration and gravity on infradiaphragmatic venous flow in normal and Fontan patients. Circulation 2000;102:III148-53.
9. Gewillig MH, Lundström UR, Bull C, Wyse RK, Deanfield JE. Exercise responses in patients with congenital heart disease after fontan repair: Patterns and determinants of performance. J Am Coll Cardiol 1990;15:1424-32.
10. Lambert E, d’Udekem Y, Cheung M, et al. Sympathetic and vascular dysfunction in adult patients with Fontan circulation. Int J Cardiol 2013;167:1333-8.
11. Driscoll DJ, Staats BA, Heise CT, et al. Functional single ventricle: cardiorespiratory response to exercise. J Am Coll Cardiol 1984;4:337-42.
12. Ohuchi H, Ohashi H, Takasugi H, Yamada O, Yagihara T, Echigo S. Restrictive ventilatory impairment and arterial oxygenation characterize rest and exercise ventilation in patients after fontan operation. Pediatr Cardiol 2004;25:513-21.
13. Mancini DM, Eisen H, Kussmaul W, Mull R, Edmunds LH Jr, Wilson JR. Value of peak exercise oxygen consumption for optimal timing of cardiac transplantation in ambulatory patients with heart failure. Circulation 1991;83:778-86.
14. Driscoll DJ, Durongpisitkul K. Exercise testing after the Fontan operation. Pediatr Cardiol 1999;20:57-9; discussion 60.
15. Durongpisitkul K, Driscoll DJ, Mahoney DW, et al. Cardiorespiratory response to exercise after modified Fontan operation: determinants of performance. J Am Coll Cardiol 1997;29:785-90.
16. Harrison DA, Liu P, Walters JE, et al. Cardiopulmonary function in adult patients late after Fontan repair. J Am Coll Cardiol 1995;26:1016-21.
17. Cooper DM, Leu SY, Taylor-Lucas C, Lu K, Galassetti P, Radom-Aizik S. Cardiopulmonary exercise testing in children and adolescents with high body mass index. Pediatr Exerc Sci 2016;28:98-108.
18. Butts RJ, Spencer CT, Jackson L, et al. Estimating equations for cardiopulmonary exercise testing variables in Fontan patients: derivation and validation using a multicenter cross-sectional database. Pediatr Cardiol 2015;36:393-401.
19. Giardini A, Hager A, Pace Napoleone C, Picchio FM. Natural history of exercise capacity after the Fontan operation: a longitudinal study. Ann Thorac Surg 2008;85:818-21.
20. Udholm S, Aldweib N, Hjortdal VE, Veldtman GR. Prognostic power of cardiopulmonary exercise testing in Fontan patients: a systematic review. Open Heart 2018;5:e000812.
21. Cunningham JW, Nathan AS, Rhodes J, Shafer K, Landzberg MJ, Opotowsky AR. Decline in peak oxygen consumption over time predicts death or transplantation in adults with a Fontan circulation. Am Heart J 2017;189:184-92.
22. Diller GP, Giardini A, Dimopoulos K, et al. Predictors of morbidity and mortality in contemporary Fontan patients: results from a multicenter study including cardiopulmonary exercise testing in 321 patients. Eur Heart J 2010;31:3073-83.
23. Egbe AC, Driscoll DJ, Khan AR, et al. Cardiopulmonary exercise test in adults with prior Fontan operation: the prognostic value of serial testing. Int J Cardiol 2017;235:6-10.
24. Nathan AS, Loukas B, Moko L, et al. Exercise oscillatory ventilation in patients with Fontan physiology. Circ Heart Fail 2015;8:304-11.
25. Goldberg DJ, Avitabile CM, McBride MG, Paridon SM. Exercise capacity in the Fontan circulation. Cardiol Young 2013;23:824-30.
26. Fernandes SM, Alexander ME, Graham DA, et al. Exercise testing identifies patients at increased risk for morbidity and mortality following Fontan surgery. Congenit Heart Dis 2011;6:294-303.
27. Goldberg DJ, Zak V, Goldstein BH, et al. Pediatric Heart Network Investigators. Results of the FUEL trial. Circulation 2020;141:641-51.
28. Baba R, Kubo N, Morotome Y, Iwagaki S. Reproducibility of the oxygen uptake efficiency slope in normal healthy subjects. J Sports Med Phys Fitness 1999;39:202-6.
29. Hollenberg M, Tager IB. Oxygen uptake efficiency slope: an index of exercise performance and cardiopulmonary reserve requiring only submaximal exercise. J Am Coll Cardiol 2000;36:194-201.
30. Bongers BC, Hulzebos HJ, Blank AC, van Brussel M, Takken T. The oxygen uptake efficiency slope in children with congenital heart disease: construct and group validity. Eur J Cardiovasc Prev Rehabil 2011;18:384-92.
31. Giardini A, Specchia S, Gargiulo G, Sangiorgi D, Picchio FM. Accuracy of oxygen uptake efficiency slope in adults with congenital heart disease. Int J Cardiol 2009;133:74-9.
32. Chen CA, Chen SY, Chiu HH, et al. Prognostic value of submaximal exercise data for cardiac morbidity in Fontan patients. Med Sci Sports Exerc 2014;46:10-5.
33. Arena R, Myers J, Abella J, et al. Prognostic value of timing and duration characteristics of exercise oscillatory ventilation in patients with heart failure. J Heart Lung Transplant 2008;27:341-7.
34. Leite JJ, Mansur AJ, de Freitas HF, et al. Periodic breathing during incremental exercise predicts mortality in patients with chronic heart failure evaluated for cardiac transplantation. J Am Coll Cardiol 2003;41:2175-81.
35. Guazzi M, Raimondo R, Vicenzi M, et al. Exercise oscillatory ventilation may predict sudden cardiac death in heart failure patients. J Am Coll Cardiol 2007;50:299-308.
36. Muneuchi J, Joo K, Yamamura K, et al. Exertional oscillatory ventilation during cardiopulmonary exercise test in Fontan patients with total cavopulmonary connection. Pediatr Cardiol 2009;30:452-7.
37. Paridon SM, Mitchell PD, Colan SD, et al. Pediatric Heart Network Investigators. A cross-sectional study of exercise performance during the first 2 decades of life after the Fontan operation. J Am Coll Cardiol 2008;52:99-107.
